Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Induction of the disease has been associated with viral processes, solar irradiation. Jan 11, 2019 reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Reticular erythematous mucinosis syndrome with telangiectasias ayse serap karadag 1, gulcin guler simsek 2 1 department of dermatology, ankara kecioren research and training hospital, ankara, turkey 2 department of pathology, ankara kecioren research and. It is a disease that tends to affect women in the third and fourth decades of life 187 see also. Reticular erythematous mucinosis definition of reticular. Examination of biopsy specimen showed focal mucin deposition in papillary and upper reticular dermis. Is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist. Characteristic findings on physical examination reticular. There was some relation to sun exposure, but the full spectrum of xenon. These are most commonly seen on the chest and upper back.
Cutaneous mucinosis in mixed connective tissue disease. The study of reticular erythematous mucinosis has been mentioned in research publications which can be found using our bioinformatics tool below. The area is photosensitive and has been present for 1 year without resolution and without new lesions. Llinear morphea with secondary mucinosisinear morphea. Clinical features and efficacy of antimalarial treatment. Background reticular erythematous mucinosis rem syndrome is a rare cutaneous disease that predominantly affects the chest and upper back area of middleaged women.
Reticular erythematous mucinosis pathology dermnet nz. Puede ser unico sin ninguna anomalia sistemica o multiple. Investigations including hematological, biochemical, serum and urine protein electrophoresis, thyroid function tests and antinuclear antibody ana were normal. A diagnosis of reticular erythematous mucinosis may involve. Clinically it is presented as an asymptomatic elevation, of firm consistency, more frequently localized in the gum or alveolar mucous. Treatment of reticular erythematous mucinosis with uva1. Reticular erythematous mucinosis rem, rem syndrome. Reticular erythematous mucinosis rem is a rare disorder with an unknown etiology. Researched pathways related to reticular erythematous mucinosis include pathogenesis, cell adhesion, immune response, response to interleukin1, photoprotection. Reticular erythematous mucinosis is a chronic and rare syndrome of unknow aetiology that affects young adult and midleaged women.
By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them. Papulonodular mucinosis in systemic lupus erythematosus. Reticular erythematous mucinosis rem is characterized by persistent, mildly pruritic, reticulated erythematous macules, papules or urticarial plaques that most often occur on the upper back and chest figure 1. What you should be alert for in the history a history of photosensitivity is commonly elicited. It has been related to sun exposure, hormonal alterations, rheumatological processes and breast cancer. Chloroquine diphosphate was introduced 250 mg day and the.
Reticular erythematous mucinosis rem, rem syndrome, plaque. We use cookies to give you the best possible experience on our website. It is also called midline mucinosis or plaquelike cutaneous mucinosis. Dermis mucinose eritematosa reticulada information on. She has been on topical and oral steroids without resolution. This report concerns two cases of cutaneous mucinosis in patients with mixed connective tissue disease in remission. Llinear morphea with secondary mucinosisinear morphea with.
The alcianblue and the pas staining revealed interstitial mucinosis in the reticular dermis. Adult variant of selfhealing cutaneous mucinosis in a. Mucinosis eritematosa reticular reticular erythematous mucinosis. Rem requires both a clinical and a pathological diagnosis. Dermis mucinose eritematosa reticulada information on the. It is a disease that tends to affect women in the third and fourth decades of life. Papulonodular mucinosis in systemic lupus erythematosus victoria g ortiz md a, ravi s krishnan md a, ling l chen md b, and sylvia hsu md a dermatology online journal 10 2. Researched pathways related to reticular erythematous mucinosis include pathogenesis, cell adhesion, immune response, response to.
Is there a home remedy for reticular erythematous mucinosis. Jun 17, 2012 cutaneous mucinosis is a group of conditions involving an accumulation of mucin or glycosaminoglycan in the skin and its annexes. Dermis sindrome rem o mucinosis reticular eritematosa. These are the first cases of mucinosis described in mixed connective tissue disease. Multiple relevant associations and triggers are known. Induction of the disease has been associated with viral processes, solar irradiation, specific. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective treatment modalities have been encouraging. Reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Aug 01, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. An accurate patient diagnosis contributes for the correct treatment. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. He had a voluminous mass with an edema aspect, a smooth. Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back.
Mucinosis eritematosa reticular actas dermosifiliograficas. Mucinosis in the oral cavity are not frequent and until this date 38 cases have been reported in literature. Cutaneous mucinosis in mixed connective tissue disease ncbi. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaquelike mucinosis and midline mucinosis. Although the exact etiology remains undefined, efforts to. Clinical practice guidelines for the management of candidiasis. The injuries of follicular mucinosis usually are located in head or more rarely to become general to neck, trunk and extremities. Sindrome rem associada a lupus eritematoso sistemico e. Reticular erythematous mucinosis is a chronic and rare syndrome of unknow. Although antimalarial treatment is generally considered the most effective approach, only a few case reports exist on its use in rem syndrome. The healthcare provider may note the characteristic skin rashes a skin biopsy of the affected region, where the tissue is examined by a pathologist under the microscope. Articulo original complicaciones en pacientes con lupus. Since it was not possible to relate these findings to any known syndrome, a combination of the main signs, reticular erythema and mucinosis, was used to name this entity rem syndrome. It is described in some connective tissue diseases but never in association with mixed connective tissue disease.
Lesiones arciformes migratorias palpables asocolderma revista. Cutaneous lupus mucinosis also known as papular and nodular mucinosis in lupus erythematosus, papular and nodular mucinosis of gold, and papulonodular mucinosis in lupus erythematosus is a cutaneous condition characterized by lesions that present as asymptomatic skincolored, at times reddish, 0. Jan 06, 2010 reticular erythematous mucinosis syndrome with telangiectasias ayse serap karadag 1, gulcin guler simsek 2 1 department of dermatology, ankara kecioren research and training hospital, ankara, turkey 2 department of pathology, ankara kecioren research and training hospital, ankara, turkey. Pappas pg, kauffman ca, andes d, benjamin dk jr, calandra tf, edwards je jr, et al. Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. Lesiones arciformes migratorias palpables asocolderma. There is a third group of lm that does not have the criteria for either scleromyxedema or the localized form called atypical group. Cutaneous mucinosis is a group of conditions involving an accumulation of mucin or glycosaminoglycan in the skin and its annexes. Mar 26, 2010 is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. A physical examination and evaluation of complete medical history. This is a 28 year old woman who presents with a reticulated rash on her chest.
Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides. A lm case, in its localized form, is described on the face of a male. Assoc prof patrick emanuel, dermatopathologist, auckland, new zealand, 2014. Reticular erythematous mucinosis or rem is a rare dermatosis characterised by papules and plaques on the upper trunk which often coalesce into a reticulated pattern.
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